HADHSC 抗体-HADHSC Antibody代理/参数/厂家-一抗-开云·官方站线上登录平台入口

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背景资料: FUNCTION: Plays an essential role in the mitochondrial β-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

DISEASE: Defects in HADHSC are the cause of 3-α-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.

保存建议: HADHSC antibody can be stored at 4˚C for short term (weeks). Long term storage should be at -20˚C. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

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